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·
Liang L,
Macdonald K, Schwiebert EM, Zeitlin PL, & Guggino
WB (2009). Spiperone, identified through
compound screening, activates calcium-dependent
chloride secretion in the airway. Am J Physiol
Cell Physiol 296, C131-C141.
·
Cebotaru
L, Vij N, Ciobanu I, Wright J, Flotte T, &
Guggino WB (2008). The cystic fibrosis
transmembrane regulator missing the first four
transmembrane segments increases wild type and
DeltaF508 processing. J Biol Chem. 283,
21926-21933.
·
Krasnov
KV, Tzetis M, Cheng J, Guggino WB, & Cutting
GR (2008). Localization studies of rare missense
mutations in cystic fibrosis transmembrane
conductance regulator (CFTR) facilitate
interpretation of genotype-phenotype relationships.
Hum Mutat 29, 1364-1372.
·
Lassance
RM, Passaro CP, Martini SV, Castiglione RC,
Gutierrez TM, Abreu SC, Antunes MA, Xisto DG,
Cebotaru L, Petrs-Silva H, Zin WA, Guggino WB,
Linden R, Rocco PR, & Morales MM (2008). Does the
use of recombinant AAV2 in pulmonary gene therapy
damage lung function? Respir Physiol Neurobiol
160, 91-98.
·
Souza-Menezes
J, Tukaye DN, Novaira HJ, Guggino WB, &
Morales MM (2008). Small nuclear RNAs U11 and U12
modulate expression of TNR-CFTR mRNA in mammalian
kidneys. Cell Physiol Biochem 22,
93-100.
·
Wright J,
Morales MM, Sousa-Menzes J, Ornellas D, Sipes J, Cui
Y, Cui I, Hulamm P, Cebotaru V, Cebotaru L,
Guggino WB, & Guggino SE (2008). Transcriptional
adaptation to Clcn5 knockout in proximal tubules of
mouse kidney. Physiol Genomics 33,
341-354.
·
Fischer
AC, Smith CI, Cebotaru L, Zhang X, Askin FB, Wright
J, Guggino SE, Adams RJ, Flotte T, & Guggino WB
(2007). Expression of a truncated cystic fibrosis
transmembrane conductance regulator with an
AAV5-pseudotyped vector in primates. Mol Ther
15, 756-763.
·
Kwon SH,
Pollard H, & Guggino WB (2007). Knockdown of
NHERF1 Enhances Degradation of Temperature Rescued
DeltaF508 CFTR from the Cell Surface of Human Airway
Cells. Cell Physiol Biochem 20,
763-772.
·
Liu X,
Luo M, Trygg C, Yan Z, Lei-Butters DC, Smith CI,
Fischer AC, Munson K, Guggino WB, Bunnell BA,
& Engelhardt JF (2007). Biological Differences in
rAAV Transduction of Airway Epithelia in Humans and
in Old World Non-human Primates. Mol Ther.
15, 2114-2123.
·
Souza-Menezes J, Morales MM, Tukaye DN, Guggino SE,
& Guggino WB (2007). Absence of ClC5 in
knockout mice leads to glycosuria, impaired renal
glucose handling and low proximal tubule GLUT2
protein expression. Cell Physiol Biochem
20, 455-464.
·
Wolde M,
Fellows A, Cheng J, Kivenson A, Coutermarsh B,
Talebian L, Karlson K, Piserchio A, Mierke DF,
Stanton BA, Guggino WB, & Madden DR (2007).
Targeting CAL as a negative regulator of
DeltaF508-CFTR cell-surface expression: an RNA
interference and structure-based mutagenetic
approach. J Biol Chem 282, 8099-8109.
·
Beitz E,
Liu K, Ikeda M, Guggino WB, Agre P, & Yasui M
(2006). Determinants of AQP6 trafficking to
intracellular sites versus the plasma membrane in
transfected mammalian cells. Biol Cell 98,
101-109.
·
Boyle MP,
Enke RA, Reynolds JB, Mogayzel PJ, Jr., Guggino
WB, & Zeitlin PL (2006). Membrane-associated
heparan sulfate is not required for rAAV-2 infection
of human respiratory epithelia. Virol J 3,
29.
·
Cai H,
Cebotaru V, Wang YH, Zhang XM, Cebotaru L, Guggino
SE, & Guggino WB (2006). WNK4 kinase
regulates surface expression of the human sodium
chloride cotransporter in mammalian cells. Kidney
Int 69, 2162-2170.
·
Caruso-Neves
C, Pinheiro AA, Cai H, Souza-Menezes J, & Guggino
WB (2006). PKB and megalin determine the
survival or death of renal proximal tubule cells.
Proc Natl Acad Sci U S A. 103,
18810-18815.
·
Guggino
WB
& Stanton BA (2006). New insights into cystic
fibrosis: molecular switches that regulate CFTR.
Nat Rev Mol Cell Biol 7, 426-436.
·
Ikeda M,
Fong P, Cheng J, Boletta A, Qian F, Zhang XM, Cai H,
Germino GG, & Guggino WB (2006). A regulatory
role of polycystin-1 on cystic fibrosis
transmembrane conductance regulator plasma membrane
expression. Cell Physiol Biochem 18,
9-20.
·
Novaira
HJ, Ornellas DS, Ortiga-Carvalho TM, Zhang XM,
Souza-Menezes J, Guggino SE, Guggino WB, &
Morales MM (2006). Atrial natriuretic peptide
modulates cystic fibrosis transmembrane conductance
regulator chloride channel expression in rat
proximal colon and human intestinal epithelial
cells. J Endocrinol 189, 155-165.
·
Pollard
HB, Eidelman O, Jozwik C, Huang W, Srivastava M, Ji
XD, McGowan B, Norris CF, Todo T, Darling T,
Mogayzel PJ, Zeitlin PL, Wright J, Guggino WB,
Metcalf E, Driscoll WJ, Mueller G, Paweletz C, &
Jacobowitz DM (2006). De novo biosynthetic profiling
of high abundance proteins in cystic fibrosis lung
epithelial cells. Mol Cell Proteomics 5,
1628-1637.
·
van den
Hove MF, Croizet-Berger K, Jouret F, Guggino SE,
Guggino WB, Devuyst O, & Courtoy PJ (2006). The
loss of the chloride channel, ClC-5, delays apical
iodide efflux and induces a euthyroid goiter in the
mouse thyroid gland. Endocrinology 147,
1287-1296.
·
Wright JM,
Merlo CA, Reynolds JB, Zeitlin PL, Garcia JG,
Guggino WB, & Boyle MP (2006). Respiratory
epithelial gene expression in patients with mild and
severe cystic fibrosis lung disease. Am J Respir
Cell Mol Biol 35, 327-336.
·
Caruso-Neves
C, Kwon SH, & Guggino WB (2005). Albumin
endocytosis in proximal tubule cells is modulated by
angiotensin II through an AT2 receptor-mediated
protein kinase B activation. Proc Natl Acad Sci U
S A. 29, 17513-17518.
·
Cebotaru
V, Kaul S, Devuyst O, Cai H, Racusen L, Guggino
WB, & Guggino SE (2005). High citrate diet
delays progression of renal insufficiency in the
ClC-5 knockout mouse model of Dent's disease.
Kidney Int 68, 642-652.
·
Cheng J,
Wang H, & Guggino WB (2005). Regulation of
cystic fibrosis transmembrane regulator trafficking
and protein expression by a Rho family small GTPase
TC10. J Biol Chem 280, 3731-3739.
·
Flotte TR,
Schwiebert EM, Zeitlin PL, Carter BJ, & Guggino
WB (2005). Correlation between DNA transfer and
cystic fibrosis airway epithelial cell correction
after recombinant adeno-associated virus serotype 2
gene therapy. Hum Gene Ther 16,
921-928.
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